A Case of Isolated Craniofacial Fibrous Dysplasia - Radiologist's Perspective

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Authors

  • P. Regu
     Department of Oral Medicine and Radiology, Tamil Nadu Government Dental College and Hospital, Chennai 600003 ,IN
  • S. Jayachandran
     Department of Oral Medicine and Radiology, Tamil Nadu Government Dental College and Hospital, Chennai, 600003 ,IN
  • P. K. Meenapriya
     Department of Oral Medicine and Radiology, Tamil Nadu Government Dental College and Hospital, Chennai 600003 ,IN

Keywords:

Fibrous Dysplasia, Craniofacial Type, Fibro Osseous Lesion, Mccuneealbright Syndrome, Radiographic Assessment
Oral Medicine and Radiology

Abstract

Fibrous dysplasia is a disease characterized by replacement of bone by fibro osseous tissue. FD has four different disease patterns. They are monostotic, polyostotic and McCunee Albright syndrome. Craniofacial pattern of disease occurs in 10-25% of patients with monostotic form and in 50% with polyostotic form. It also occurs as isolated craniofacial form. In isolated variety no extracranial lesions are present. Radiographic diagnosis plays an important role in diagnosis, classification and assessing prognosis of fibrous dysplasia. In this paper we report a case of isolated craniofacial type of fibrous dysplasia in a young female patient involving the maxilla and skull bones with a complete radiographic CT assessment of the extent of the lesion. Temporal bone involvement and bilateral lesion in certain cranial bones are the rare findings noted in this case.

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Published

2018-09-12

How to Cite

Regu, P., Jayachandran, S., & Meenapriya, P. K. (2018). A Case of Isolated Craniofacial Fibrous Dysplasia - Radiologist’s Perspective. Journal of Pierre Fauchard Academy (India Section), 28(1), 5–10. Retrieved from https://informaticsjournals.co.in/index.php/jpfa/article/view/22218

Issue

Volume 28, Issue 1, March 2014

Section

Original Articles

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All the articles published in JPFA are distributed under a creative commons license. The journal allows the author(s) to hold the copyright of their work (all usages allowed except for commercial purpose).

 

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